Ričardas Kundelis1, Laura Dobrovaitė1, Mažvydas Užkurnys1
1 Lithuanian University of Health Sciences, Academy of Medicine, Faculty of Medicine, Kaunas, Lithuania
ABSTRACT
Bronchopulmonary sequestration is an uncommon congenital anomaly in which part of the non‐functioning pulmonary tissue is divided from the normal lung and has no normal connection with the tracheobronchial tree and pulmonary artery. This disease has an unknown etiology and is representing 0,1-6% of all structural lung diseases and developmental malformations. Diagnosis and management of congenital lung malformations has evolved over the past several decades. Earlier, more definitive diagnoses and, consequently, more timely intervention in utero or after birth have been enabled by advancement in imaging technology. The most commonly used imaging techniques to identify and characterize sequestration spectrum are conventional computer tomography and angiography. Aim: To present a clinical case of bronchopulmonary sequestration diagnosed in Hospital of Lithuanian University of Health Sciences Kaunas Clinics and review the latest scientific literature on this topic. Methods: A review of the literature using the PubMed database was performed. Publications, researching the problem of pulmonary malformations, were selected and a clinical case of bronchopulmonary sequestration was presented. Conclusions: Pulmonary sequestration is uncommon disease, representing about 1 to 6% of all congenital lung anomalies and might be undetected during the prenatal period and early childhood years. If PS remains undiagnosed the risk of massive hemoptysis from pulmonary hypertension arises. Our purpose is to promote awareness of diagnosing this condition among various physicians. In this article we present a clinical case of bronchopulmonary sequestration with imaging characteristics.
Keywords: pulmonary sequestration, lung malformations, anomalous systemic arterial supply.